Dentinogenesis imperfecta type II: a case report

Dentinogenesis Imperfecta is one of the most common autosomal dominant hereditary disorders of dentin formation. It is classified as, type I which is associated with osteogenesis imperfecta; type II not associated with osteogenesis imperfecta; and Type III is associated with the Brandywine triracial isolate.Clinically the teeth shows discolouration and often results in shearing of the overlying enamel which results in attrition and fracture. Radiographically it shows structural defects such as bulbous crowns and small pulp chambers. Early diagnosis and treatment can achieve better functional and aesthetic results and psychological benefit. Inthis case report we present a 27 year old female with generalized brownish discolouration of the teethand severe attrition with radiographic features of bulbous crown and spike shaped roots suggestive of Dentinogenesis Imperfecta type II and the literature including etiology and management is briefly reviewed.