Robinow Syndrome: Medical And Stomatological Considerations For Comprehensive Patient Management

Introduction: Robinow's Syndrome (RS) is a rare, skeletal malformation occurs that can also affect other organs, t in a wide spectrum of clinical characteristics, which can be: craniofacial, dental, musculoskeletal, urogenital and presence of systemic complications. Objective: to make considerations about systemic alterations, to identify the general characteristics, oral diseases in Robinow Syndrome and additionally to report a clinical case of a patient with this syndrome, highlighting aspects of dental interest. Case Report: It was observed in the evaluation and monitoring of the patient the following characteristics general: short stature, fetal face, exophthalmos, hypertelorism, cognitive impairment, skeletal abnormalities, renal impairment, cognitive impairments. The patient is followed up dentally since he was a baby and the following oral characteristics were present: malocclusion, deep palate, crowding , unilateral posterior crossbite, gingival hyperplasia, difficulty in cleaning, nausea during the dental approach, but with satisfactory quality of oral health op atient reported is male, 12 years old, with diagnosis of S R. Conclusion: Approach and comprehensive treatment should be encouraged, and monitoring by a multiprofessional team, as these individuals have complex problems in relation to systemic, behavioral and dental characteristics. The Early dental care to these patients should be performed so that do not require complex and invasive dental treatments due to systemic and cognitive impairment.